Congenital Glenoid Hypoplasia

This malformation is due to failure of formation of the lower and upper glenoid epiphysis. It is characterized in the radiogram by flattening, shallowness, and a denate appeareance of the glenoid cavity.

The lower aspect of the clavicle may be hypertrophied into a bony prominence, and there may be spina bifida in the cervical region.

Often, the abnormality is bilateral and is encountered as an isolated malformation. It may be hereditary. Samilson reported congenital glenoid hypoplasia in three successive generations of the same family.

Occasionally, it is seen in association with other congenital malformations such as Apert’s syndrome, Hurler’s syndrome, aglossia-adactylia, oculodento-osseous dysplasia, Holt-Oram syndrome, and Cornelia De Lange’s syndrome. [Read more...]

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